ASYMPTOMATIC PHEOCHROMOCYTOMA ASSOCISATED WITH VON RECKLINGHAUSEN’S DISEASE (NEUROFIBROMATOSIS TYPE1): CASE REPORT

Abstract

We report a case of 50 years old male with neurofibromatosis complaining of recurrent attacks of right loin pain. Clinically , the patient was normotensive, his body was full of neurofibromas with cafe au lait patches. Catecholamine in urine was markedly elevated. No other endocrinological abnormality depicted. CT scan abdomen revealed presence of right adrenal mass 5.9X5.9 cm with central necrosis and haemorrage. I 131 metaiodobenzylguanidine (I 131-MIBG) revealed a well defined sizable area of intense tracer accumulation at right suprarenal gland. The patient was operated upon and the histopathology proved to be benign pheochromocytoma.